119: 3-HYDROXY 3-METHYL-GLUTARYLCO-ALYASE DEFICIENCY
نویسندگان
چکیده
منابع مشابه
3-hydroxy-3-methylglutaryl-CoA synthase deficiency
Deficiency of mitochondrial 3-hydroxy-3-methylglutaryl-CoA synthase, the rate-limiting enzyme in hepatic ketogenesis, causes potentially life-threatening hypoglycemic hypoketotic coma during fasting periods. In the normal, nonfasting state, patients are completely asymptomatic and show no abnormalities in standard metabolic tests. As a consequence, diagnosing 3-hydroxy-3-methylglutaryl-CoA synt...
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The CHCl3-soluble extract of Piper guanacastensis (Piperaceae) was found to have noteworthy insecticidal activity to Aedes atropalpus mosquito larvae (LC50 80.5 micrograms/mL). Bioassay-guided fractionation afforded methyl 4-hydroxy-3-(3'-methyl-2'-butenyl)benzoate (1) as the major bioactive constituent (LC50 20.5 micrograms/mL). The separation of compound 1 from its transesterification artifac...
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25 26 Hydroxycarbonyl compounds are important secondary reaction products in the 27 oxidation of Volatile Organic Compounds (VOCs) in the atmosphere. The 28 atmospheric fate of these oxygenated VOCs is however poorly understood, 29 especially the relevance of the photolytic pathway. In this work, a combined 30 investigation of the photolysis and temperature-dependent OH radical reaction of 331 ...
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BACKGROUND Atherosclerotic cardiovascular diseases are the leading cause of death in the United States. A reduction in cholesterol with 3-hydroxy-3-methyl-glutaryl-CoA reductase inhibitors (statin) significantly reduces mortality and morbidity. Statins may be associated with cognitive impairment or dementia. Our aim was to study the association of cognitive impairment or dementia in patients wh...
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ژورنال
عنوان ژورنال: Pediatric Research
سال: 1988
ISSN: 0031-3998,1530-0447
DOI: 10.1203/00006450-198808000-00144